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Author: R. Salvayre
Publisher: Springer Science & Business Media
ISBN: 1461310296
Category : Science
Languages : en
Pages : 791
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Book Description
This book presents the proceedings of the meeting on "Lipid Storage Disorders" which took place in Toulouse, France, in September 14-18, 1987 and which was set up as a joint NATO Advanced Research Workshop and INSERM International Symposium. The meeting probably was the first truly international symposium devoted entirely to basic as well as applied aspects of lipid metabolism as related to the lipid storage disorders. Participants came from Europe, USA, Israel and Japan, and presented data on research in molecular biology and genetics, enzymology, cell biology as well as medical and epidemiological aspects of normal and pathological lipid metabolism. In the latter case, special attention was directed to the lysosomal B-glucosidase in relation to Gaucher disease and to sphin gomyelinase in relation to Niemann-Pick disease, and "two round" table discussions were devoted to the two respective items. But research on many other lipidoses was presented, as lectures or posters and avidly discussed. Other topics presented in special sessions were drug induced lipidoses and peroxisomal disorders. The meeting ended with a session devoted to medical aspects of disorders of lipid metabolism. The symposium which included about 50 lectures and close to 70 posters had an intense scientific character superimposed on a most pleasant and collegial atmosphere. Ample time was provided to personal discussions ; lodging of the participants in the students' residence located near the meeting place, permitted further contacts between them.
Author: R. Salvayre
Publisher: Springer Science & Business Media
ISBN: 1461310296
Category : Science
Languages : en
Pages : 791
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Book Description
This book presents the proceedings of the meeting on "Lipid Storage Disorders" which took place in Toulouse, France, in September 14-18, 1987 and which was set up as a joint NATO Advanced Research Workshop and INSERM International Symposium. The meeting probably was the first truly international symposium devoted entirely to basic as well as applied aspects of lipid metabolism as related to the lipid storage disorders. Participants came from Europe, USA, Israel and Japan, and presented data on research in molecular biology and genetics, enzymology, cell biology as well as medical and epidemiological aspects of normal and pathological lipid metabolism. In the latter case, special attention was directed to the lysosomal B-glucosidase in relation to Gaucher disease and to sphin gomyelinase in relation to Niemann-Pick disease, and "two round" table discussions were devoted to the two respective items. But research on many other lipidoses was presented, as lectures or posters and avidly discussed. Other topics presented in special sessions were drug induced lipidoses and peroxisomal disorders. The meeting ended with a session devoted to medical aspects of disorders of lipid metabolism. The symposium which included about 50 lectures and close to 70 posters had an intense scientific character superimposed on a most pleasant and collegial atmosphere. Ample time was provided to personal discussions ; lodging of the participants in the students' residence located near the meeting place, permitted further contacts between them.
Author: G. Schettler
Publisher: Springer Science & Business Media
ISBN: 3642873677
Category : Medical
Languages : en
Pages : 637
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Book Description
Advances which have been made in the field of lipid chemistry and bio chemistry during the last ten years mainly are the results of progress in metho dology. The introduction of isotopic and chromatographic techniques has not only enriched our knowledge of normal lipid metabolism but has also greatly enhanced the understanding of the various lipidoses. This is well illustrated by a comparison of the contents of the present monograph with those of my 1955 review in Handbuch der Inneren Medizin (Springer). In addition to better information about the classic lipid thesaurismoses Nie mann-Pick disease, Gaucher's disease and Tay-Sachs disease, the number of hereditary lipid storage diseases has increased considerably through the recogni tion of new syndromes such as metachromatic leukodystrophy, Fabry's disease, Refsum's disease (heredopathia atactica polyneuritiformis), a-p-lipoproteinemia, and Tangier disease. Conversely, disorders such as Hand-Scholler-Christian disease which has been considered a lipidosis up to 1958 (THANNHAUSER) must now be differentiated from the hereditary disturbances of lipid metabolism. Essential hyperlipemia which at one time seemed to be a well defined entity has now been recognized to consist of a number of subgroups, whose pathogeneses appear to be quite different, and whose classification is by no means definite. Similar problems exist for "essential hypercholesterolemia". Since the knowledge of today is the key for the solutions of tomorrow, we are fortunate that the chapters on lipidoses are supplemented by a comprehensive account of lipid chemistry and biochemistry which has been coordinated by W. STOFFEL.
Author: Siegfried Josef Thannhauser
Publisher:
ISBN:
Category : Biochemistry
Languages : en
Pages : 626
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Book Description
Author: Joseph Bernsohn
Publisher:
ISBN:
Category : Medical
Languages : en
Pages : 336
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Book Description
Glossy publication advertising the commercial photographs of Getty Images, showing very high quality images of sporting moments and events, and of entertainment and news stories.
Author: Siegfried Thannhauser
Publisher:
ISBN:
Category : Biochemistry
Languages : en
Pages : 628
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Book Description
Author: Mihra S. Taljanovic
Publisher: Oxford University Press, USA
ISBN: 019093817X
Category : Medical
Languages : en
Pages : 439
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Book Description
Musculoskeletal Imaging Volume 2 summarizes the key information related to metabolic, infectious and congenital diseases; internal derangement of the joints; and arthrography and ultrasound. Succinct, structured overviews of each pathology are ideal for use by radiology residents during their musculoskeletal rotations and for residents, fellows, and practicing radiologists for board exam preparation or for daily clinical reference.
Author: Bruno Volk
Publisher: Springer Science & Business Media
ISBN: 1468477358
Category : Medical
Languages : en
Pages : 603
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Book Description
The present volume contains the scientific contributions to the Fifth International Symposium on "Current Trends in Sphingo lipidoses and Allied Disorders" under the auspices of the Isaac Albert Research Institute of the Kingsbrook Jewish Medical Center, the Department of Pathology, Downstate Medical Center, State Uni versity of New York, Brooklyn, New York, and the National Tay-Sachs and Allied Diseases Association, Inc., New York. A review of the four previous Symposia shows the increase in scope of the scientific exploration in this rapidly expanding field. The first meeting, held in 1958, was devoted to the discussion al most entirely of Tay-Sachs disease. The majority of the work emanated from local laboratories. The participants at the present Symposium came from many other domestic and foreign research in stitutions. The scope of the papers presented at these meetings and the interest shown in the Symposium demonstrates the signifi cance attached by the scientific community to the problems of these hereditary diseases. The reasons for this are apparent, when one considers the contributions during recent years to our basic know ledge by lipid and enzyme chemistry, genetics, and neuropathology. Partly because of the hereditary nature of these diseases any new discovery in this field has general meaning and permits cautious generalization well beyond its clinical significance.
Author: Gunter Schlierf
Publisher:
ISBN: 9783642873683
Category :
Languages : en
Pages : 644
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Book Description
Author: Peter Schwandt
Publisher: Warren H. Green
ISBN:
Category : Medical
Languages : en
Pages : 200
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Book Description
Author: Joseph Bernsohn
Publisher:
ISBN:
Category : Lipidoses
Languages : en
Pages : 316
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Book Description
